Intrahepatic Gall Bladder with Choledochal Cyst with Malrotation of Gut – A Rare Association

Choledochal Cysts are rare cystic dilatory conditions of the biliary tree with malignant tendency. These are more frequently reported in children. Surgical removal of these cysts can significantly reduce the risk of malignancy and also reduce the associated complications. However, Choledochal Cysts have been paid lesser attention in adults. Choledochal Cysts associated with Intrahepatic gall bladder and Malrotation of the gut have rarely been reported. We herein report a case of a 15-year-old female patient with Type 4a Choledochal cyst associated with intrahepatic gall bladder and mal-rotation of the intestine which was incidentally found at surgery. The patient underwent Excision of Choledochal cyst with Cholecystectomy with Appendicectomy with Hepatico-jejunostomy with Jejuno-jejunostomy, and Ladd's procedure was simultaneously performed for asymptomatic Intestinal Malrotation.